Discussion of Dermatofibrosarcoma protuberans
- Dermatofibrosarcoma protuberans is an uncommon spindle cell tumor.
- Dermatofibrosarcoma protuberans typically arises in the dermis as a multinodular mass, which then spreads into the subcutaneous tissues and muscle.
- Males are slightly more commonly affected than females.
- The tumor occurs in patients of all ages, with the highest frequency occurring between the second and the fifth decades.
- Lesions ranging from 1 cm to more than 25 cm have been described in the literature.
- The trunk is the most common site of involvement, accounting for almost half of all cases. The extremities followed by the head and neck are the next most common sites.
- Patients often ignore these tumors because of their slow growth and they are often left untreated for many years.
- Dermatofibrosarcoma protuberans has an excellent prognosis after complete resection but has a marked tendency to recur locally if inadequate surgical resection margins are obtained.
- Metastases are rare.
 Imaging Findings for Dermatofibrosarcoma protuberans
Patient #1: CT images demonstrating a dermatofibrosarcoma protuberans in the right groin
 See Also
 External Links
 References for Dermatofibrosarcoma protuberans
- Torreggiani, William C., Al-Ismail, Khalid, Munk, Peter L., Nicolaou, Savvas, O'Connell, John X., Knowling, Margaret A. Dermatofibrosarcoma Protuberans: MR Imaging Features. Am. J. Roentgenol. 2002 178: 989-993.