Dermatofibrosarcoma protuberans

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[edit] Discussion of Dermatofibrosarcoma protuberans

  • Dermatofibrosarcoma protuberans is an uncommon spindle cell tumor.
  • Dermatofibrosarcoma protuberans typically arises in the dermis as a multinodular mass, which then spreads into the subcutaneous tissues and muscle.
  • Males are slightly more commonly affected than females.
  • The tumor occurs in patients of all ages, with the highest frequency occurring between the second and the fifth decades.
  • Lesions ranging from 1 cm to more than 25 cm have been described in the literature.
  • The trunk is the most common site of involvement, accounting for almost half of all cases. The extremities followed by the head and neck are the next most common sites.
  • Patients often ignore these tumors because of their slow growth and they are often left untreated for many years.
  • Dermatofibrosarcoma protuberans has an excellent prognosis after complete resection but has a marked tendency to recur locally if inadequate surgical resection margins are obtained.
  • Metastases are rare.


[edit] Imaging Findings for Dermatofibrosarcoma protuberans

[edit] Images

Patient #1: CT images demonstrating a dermatofibrosarcoma protuberans in the right groin

[edit] See Also

[edit] External Links

Goldminer: Dermatofibrosarcoma protuberans

[edit] References for Dermatofibrosarcoma protuberans