Ebstein's anomaly

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[edit] Discussion of Ebstein's anomaly

  • Characterized by varying degrees of dysplasia and displacement of the tricuspid valve leaflets into the right ventricle.
  • The portion of the right ventricle into which blood flows fails to function normally, and the outflow tract functions as the main pumping apparatus of the right ventricle.
  • Inferior displacement of tricuspid valve leaflets with enlargement of the right atrium and enlargement and dysfunction of the right ventricle are the classic features of Ebstein anomaly.
  • The majority of patients have a concomitant patent foramen ovale or secundum atrial septal defect.

[edit] Imaging Findings for Ebstein's anomaly

[edit] Plain film

  • Right atrial enlargement and right ventricular enlargement.
  • The aorta is small, and the pulmonary trunk, which normally appears as a discrete convex bulge, is absent.
  • The above combination of features produces a cardiac silhouette that has been described as box shaped.

[edit] CT and MRI

  • Inferior displacement of tricuspid valve leaflets with enlargement of the right atrium and enlargement and dysfunction of the right ventricle.

[edit] Images

Patient #1

[edit] See Also

[edit] External Links

[edit] References for Ebstein's anomaly