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 Discussion of Encephalocraniocutaneous lipomatosis
- Encephalocraniocutaneous Lipomatosis (ECCL) is a rare congenital neurocutaneous syndrome.
- ECCL not inherited in a mendelian fashion.
- ECCL is characterized by unilateral lipomas of the cranium, face, and neck, ipsilateral lipodermoids of the eye, and ipsilateral brain anomalies
- The clinical features of ECCL overlap with other neurocutaneous syndromes.
 Imaging Findings for Encephalocraniocutaneous lipomatosis
- Enlargement of the lateral ventricle, intracranial cysts, and the atrophy of the affected cerebral hemisphere are the most constant findings.
 See Also
 External Links
 References for Encephalocraniocutaneous lipomatosis
- Parazzini, Cecilia, Triulzi, Fabio, Russo, Gianni, Mastrangelo, Massimo, Scotti, Giuseppe. Encephalocraniocutaneous Lipomatosis: Complete Neuroradiologic Evaluation and Follow-up of Two Cases. AJNR Am J Neuroradiol 1999 20: 173-176.