Fibromuscular dysplasia

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[edit] Discussion of Fibromuscular dysplasia

  • Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disease.

[edit] Types

  • The pathological classification scheme for fibromuscular lesions is based on the arterial layer involved — intima, media, or adventitia — in which the lesion predominates, but are not mutually exclusive. FMD has been described using the terms dyplasia, fibroplasia, fibrodysplasia, and hyperplasia.
    • Intimal dysplasia
    • Medial dysplasia is the most common type (85%); causes classic stenoses alternating with aneurysms. Causes "string of beads" appearance.
    • Perimedial dysplasia
    • Medial hyperplasia
    • Adventitial (periarterial) dysplasia

[edit] Location

  • Fibromuscular dysplasia has been described in almost every arterial bed in the body.
  • Renal arteries, 60%, most common site.
  • ICA or Vertebral arteries, 35%.
  • Iliac arteries, 3%.
  • Visceral arteries, 2%.

[edit] Fibromuscular Dysplasia of the Renal Arteries

  • Renovascular fibromuscular dysplasia tends to affect women between 15 and 50 years of age.
  • Renal fibromuscular dysplasia is often discovered incidentally during the investigation of another problem.
  • Fibromuscular dysplasia accounts for less than 10 percent of cases of renovascular hypertension.
  • Treatment: Successful angioplasty often results in a substantial and rapid reduction of both the systolic and the diastolic blood pressure.

[edit] Imaging Findings for Fibromuscular dysplasia

  • Classic "string of beads" appearance on angiogram, CTA, or MRA

[edit] Images

Patient #1

[edit] External Links

Goldminer: Fibromuscular dysplasia

[edit] References for Fibromuscular dysplasia