Discussion of Mounier-Kuhn syndrome
- Mounier-Kuhn syndrome is AKA tracheobronchomegaly
- Mounier-Kuhn syndrome is a rare condition characterized by marked dilatation of the trachea and mainstem bronchi (peripheral airways are normal in caliber)
- It is associated with atrophy of cartilaginous, muscular, and elastic components of the tracheal wall and may be seen in a variety of systemic diseases resulting in connective tissue abnormalities (i.e. Ehlers-Danlos syndrome).
 Imaging Findings for Mounier-Kuhn syndrome
- CT findings include a thinning of the tracheal wall and a tracheal diameter of more than 3 cm at 2 cm above the aortic arch.
- Tracheal scalloping or frank diverticulosis can also be seen but is difficult to appreciate in cross section.
- The trachea tends to collapse with forced expiration (tracheomalacia).
 See Also
 External Links
 References for Mounier-Kuhn syndrome
- Webb, Emily M., Elicker, Brett M., Webb, W. Richard. Using CT to Diagnose Nonneoplastic Tracheal Abnormalities: Appearanceof the Tracheal Wall. Am. J. Roentgenol. 2000 174: 1315-1321.