Osteofibrous dysplasia

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[edit] Discussion of Osteofibrous dysplasia

  • Osteofibrous dysplasia is sometimes referred to as ossifying fibroma. The latter term is discouraged, as it refers also to an unrelated lesion of the mandible.
  • Osteofibrous dysplasia involves the tibia in approximately 90% of cases.
  • The lesions are usually diaphyseal, especially involving the middle to distal third of the shaft and typically involving the anterior cortex.
  • Patients present in the 1st or 2nd decade.


  • Distinction between fibrous dysplasia, adamantinoma, and osteofibrous dysplasia can be difficult.
  • Controversy does exist as to the possibility that osteofibrous dysplasia is in essence an early adamantinoma or is prone to transformation.
  • Contemporary theory would consider the two as distinct entities.
  • It has been suggested that osteofibrous dysplasia has a more favorable prognosis than either fibrous dysplasia or adamantinoma, as it exhibits a tendency toward spontaneous regression without residual skeletal deformity

[edit] Imaging Findings for Osteofibrous dysplasia

  • Diaphyseal lesion, especially involving the middle to distal third of the shaft and typically involving the anterior cortex.
  • Bowing and enlargement of the bone are typically seen, often with a characteristic adjacent sclerotic band

[edit] Images

Patient #1: Radiographs demonstrate osteofibrous dysplasia

[edit] See Also

[edit] External Links

[edit] References for Osteofibrous dysplasia