Sacrococcygeal teratoma

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[edit] Discussion of Sacrococcygeal teratoma

  • Sacrococcygeal teratoma is the most common congenital neoplasm, occurring in one in 40,000 infants.
  • Approximately 75% of affected infants are female.
  • The tumor is derived from the pluripotential cell line and contains components arising from all three germ layers.
  • Fetal sacrococcygeal teratomas diagnosed in utero carry a high risk of preterm delivery (50%), a mortality rate of 15-35%, and a morbidity rate of 12-68%.
  • The perinatal mortality and morbidity rates are high because of high output cardiac failure, preterm delivery, anemia, dystocia, and tumor rupture.
  • The intrapelvic and intraabdominal extent of the sacrococcygeal teratoma and its compressive effect on the urinary tract also affect perinatal morbidity.
  • Sacrococcygeal teratomas can grow at a very rapid rate and reach enormous volumes, which can approach and even eclipse the volume of the fetus itself.
  • Prognosis seems to be related not to the size of the mass but rather to its content and extent. Solid hypervascularized masses carry a poorer prognosis than purely cystic masses.

[edit] Imaging Findings for Sacrococcygeal teratoma

[edit] US

  • The sonographic appearance of a sacrococcygeal teratoma is typically that of a heterogeneous, mixed cystic and solid mass. The tumors may be purely cystic in 15% of cases.
  • Interrogation with Doppler US is essential to evaluate tumor vascularity.
  • The fetal spine should be meticulously evaluated for defects, as a myelomeningocele is the primary differential diagnosis. In addition, a sacrococcygeal teratoma may involve the spinal canal.

[edit] Images

Patient #1

[edit] See Also

[edit] External Links

[edit] References for Sacrococcygeal teratoma